There are four stages of lymphedema. The disease will not necessarily progress from a lower stage to a higher stage. Right now there is no cure for lymphedema, but with proper care the disease can be managed and progression can be prevented.
Stage 0 - Lymphedema is present but does not cause symptoms (subclinical). Swelling is not apparent despite reduced lymphatic function. It may exist months or years before visible swelling occurs.
Stage I - Early accumulation of fluid that is relatively high in protein content. Swelling may subside with limb elevation. Pitting of the skin may occur.
Stage II - Pitting may or may not occur as tissue fibrosis develops. Limb elevation alone rarely reduces tissue swelling.
Stage III - A severe increase in swelling may develop, along with skin changes, such as thickening of the skin, fat deposits, and warty over-growths. This stage of lymphedema may also be called lymphostatic elephantitis.